{"id":16552,"date":"2022-07-26T16:54:27","date_gmt":"2022-07-26T20:54:27","guid":{"rendered":"https:\/\/www.myface.org\/?page_id=16552"},"modified":"2022-08-02T13:03:57","modified_gmt":"2022-08-02T17:03:57","slug":"signs-symptoms","status":"publish","type":"page","link":"https:\/\/www.myface.org\/es\/craniofacial-conditions\/craniofacial-microsomia\/signs-symptoms\/","title":{"rendered":"Signs &#038; Symptoms of Craniofacial Microsomia"},"content":{"rendered":"<div class=\"wpb-content-wrapper\"><div class=\"vc_row wpb_row vc_row-fluid\"><div class=\"wpb_column vc_column_container vc_col-sm-12\"><div class=\"vc_column-inner\"><div class=\"wpb_wrapper\"><div class=\"ult-spacer spacer-69ea3fd2dfc5a\" data-id=\"69ea3fd2dfc5a\" data-height=\"80\" data-height-mobile=\"80\" data-height-tab=\"80\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"50\" style=\"clear:both;display:block;\"><\/div><div id=\"ultimate-heading-21469ea3fd2dfc89\" class=\"uvc-heading ult-adjust-bottom-margin ultimate-heading-21469ea3fd2dfc89 uvc-6604\" data-hspacer=\"no_spacer\"  data-halign=\"center\" style=\"text-align:center\"><div class=\"uvc-heading-spacer no_spacer\" style=\"top\"><\/div><div class=\"uvc-main-heading ult-responsive\"  data-ultimate-target='.uvc-heading.ultimate-heading-21469ea3fd2dfc89 h2'  data-responsive-json-new='{\"font-size\":\"desktop:46px;tablet:46px;tablet_portrait:46px;mobile_landscape:35px;mobile:35px;\",\"line-height\":\"\"}' ><h2 style=\"font-weight:bold;color:#ffffff;\">Signos y s\u00edntomas de microsom\u00eda craneofacial<\/h2><\/div><\/div><div class=\"ult-spacer spacer-69ea3fd2dfca2\" data-id=\"69ea3fd2dfca2\" data-height=\"80\" data-height-mobile=\"80\" data-height-tab=\"80\" data-height-tab-portrait=\"\" data-height-mobile-landscape=\"50\" style=\"clear:both;display:block;\"><\/div><\/div><\/div><\/div><\/div><!-- Row Backgrounds --><div class=\"upb_color\" data-bg-override=\"0\" data-bg-color=\"#00a4b4\" data-fadeout=\"\" data-fadeout-percentage=\"30\" data-parallax-content=\"\" data-parallax-content-sense=\"30\" data-row-effect-mobile-disable=\"true\" data-img-parallax-mobile-disable=\"true\" data-rtl=\"false\"  data-custom-vc-row=\"\"  data-vc=\"8.0\"  data-is_old_vc=\"\"  data-theme-support=\"enable\"   data-overlay=\"false\" data-overlay-color=\"\" data-overlay-pattern=\"\" data-overlay-pattern-opacity=\"\" data-overlay-pattern-size=\"\"    ><\/div><div class=\"vc_row wpb_row vc_row-fluid\"><div class=\"wpb_column vc_column_container vc_col-sm-8 vc_col-lg-offset-1 vc_col-lg-10 vc_col-md-offset-1 vc_col-md-10 vc_col-xs-12\"><div class=\"vc_column-inner\"><div class=\"wpb_wrapper\"><div class=\"vc_row wpb_row vc_inner vc_row-fluid\"><div class=\"wpb_column vc_column_container vc_col-sm-8\"><div class=\"vc_column-inner\"><div class=\"wpb_wrapper\">\n\t<div class=\"wpb_text_column wpb_content_element\" >\n\t\t<div class=\"wpb_wrapper\">\n\t\t\t<p><span style=\"text-decoration: underline;\"><a href=\"\/es\/\"><strong>Hogar<\/strong><\/a><\/span> &gt; <strong><span style=\"text-decoration: underline;\"><a href=\"\/es\/craniofacial-conditions\/\">Condiciones craneofaciales<\/a><\/span><\/strong> &gt; <span style=\"text-decoration: underline;\"><a href=\"\/es\/craniofacial-conditions\/craniofacial-microsomia\/\"><strong>Craniofacial Microsomia<\/strong><\/a><\/span> &gt;\u00a0<strong>Signos y s\u00edntomas<\/strong><\/p>\n\n\t\t<\/div>\n\t<\/div>\n\n\t<div class=\"wpb_text_column wpb_content_element\" >\n\t\t<div class=\"wpb_wrapper\">\n\t\t\t<h2>C\u00f3mo se desarrolla la Microsom\u00eda Craneofacial<\/h2>\n<p>Durante el desarrollo fetal, estructuras conocidas como el primer y segundo arco braquial eventualmente se desarrollar\u00e1n en la cabeza y el cuello. El desarrollo anormal de estas estructuras da como resultado las caracter\u00edsticas faciales distintivas de la microsom\u00eda craneofacial y afecciones relacionadas. La mayor\u00eda de los pacientes tienen asimetr\u00eda facial o microsom\u00eda hemifacial, donde un lado de la cara se ve diferente al otro. Esto se debe al subdesarrollo de la mand\u00edbula, los p\u00f3mulos y los m\u00fasculos faciales. Es de destacar que, aunque la microsom\u00eda hemifacial es la presentaci\u00f3n m\u00e1s com\u00fan, ambos lados de la cara pueden verse afectados hasta en 1 de cada 3 pacientes.<\/p>\n<h2>Signos y s\u00edntomas comunes que afectan las estructuras de la cabeza y el cuello<\/h2>\n<p>Adem\u00e1s de la asimetr\u00eda facial, los pacientes tambi\u00e9n suelen tener los siguientes signos y s\u00edntomas comunes que pueden afectar diferentes \u00e1reas de las estructuras de la cabeza y el cuello, incluida la cara, la mand\u00edbula, los dientes, los ojos y las orejas. , y otras estructuras de la cabeza y el cuello:<\/p>\n<p><span style=\"font-weight: 400;\">\u00a0<\/span><\/p>\n<table style=\"height: 752px;\" border=\"black\" width=\"624\">\n<tbody>\n<tr>\n<td><b>\u00c1rea afectada<\/b><\/td>\n<td><b>Signos y s\u00edntomas<\/b><\/td>\n<\/tr>\n<tr>\n<td><span style=\"font-weight: 400;\">Cara<\/span><\/td>\n<td>\n<ul>\n<li><span style=\"font-weight: 400;\">Asimetr\u00eda de la cara<\/span><\/li>\n<li><span style=\"font-weight: 400;\">M\u00fasculos faciales subdesarrollados<\/span><\/li>\n<li><span style=\"font-weight: 400;\">Da\u00f1o a los nervios faciales que dificultan la sonrisa y las expresiones<\/span><\/li>\n<li><span style=\"font-weight: 400;\">faciales Reducci\u00f3n de la grasa facial<\/span><\/li>\n<li><a href=\"https:\/\/www.myface.org\/es\/craniofacial-conditions\/cleft-lip-and-or-palate\/\"><span style=\"font-weight: 400;\">Labio leporino, paladar hendido o ambos<\/span><\/a><\/li>\n<\/ul>\n<\/td>\n<\/tr>\n<tr>\n<td><span style=\"font-weight: 400;\">Mand\u00edbula<\/span><\/td>\n<td>\n<ul>\n<li><span style=\"font-family: inherit; font-size: inherit;\">Articulaci\u00f3n de la mand\u00edbula estrecha o faltante o huesos<\/span><\/li>\n<\/ul>\n<\/td>\n<\/tr>\n<tr>\n<td><span style=\"font-weight: 400;\">Dientes<\/span><\/td>\n<td>\n<ul>\n<li><span style=\"font-weight: 400;\">Arco dental desigual que da como resultado una sonrisa torcida o dientes desalineados Dientes<\/span><\/li>\n<li><span style=\"font-weight: 400;\">peque\u00f1os, deformes o faltantes<\/span><\/li>\n<li><span style=\"font-weight: 400;\">Retraso en el desarrollo de los dientes<\/span><\/li>\n<\/ul>\n<\/td>\n<\/tr>\n<tr>\n<td><span style=\"font-weight: 400;\">O\u00eddos<\/span><\/td>\n<td>\n<ul>\n<li><span style=\"font-weight: 400;\">O\u00eddo parcialmente formado (microtia)<\/span><\/li>\n<li><span style=\"font-weight: 400;\">O\u00eddo completamente ausente (anotia)<\/span><\/li>\n<li><span style=\"font-weight: 400;\">O\u00eddo(s) deforme(s<\/span><\/li>\n<li><span style=\"font-weight: 400;\">piel (crecimientos) en el o\u00eddo y mejilla<\/span><\/li>\n<li><span style=\"font-weight: 400;\">Sordera debido a la falta del canal auditivo externo y\/o da\u00f1o al o\u00eddo medio<\/span><\/li>\n<\/ul>\n<\/td>\n<\/tr>\n<tr>\n<td><span style=\"font-weight: 400;\">Ojos<\/span><\/td>\n<td>\n<ul>\n<li><span style=\"font-weight: 400;\">Ojo(s) muy peque\u00f1o(s) o faltante(s)<\/span><\/li>\n<li><span style=\"font-weight: 400;\">Quistes dermoides epibulbares (crecimientos anormales en el su cara del ojo)<\/span><\/li>\n<li><span style=\"font-weight: 400;\">Falta de p\u00e1rpado u otro tejido<\/span><\/li>\n<\/ul>\n<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n<p>*<a href=\"https:\/\/www.nidcr.nih.gov\/health-info\/hemifacial-microsomia\">*Adaptado del Instituto Nacional de Investigaci\u00f3n Dental y Craneofacial<\/a><\/p>\n<p>Como resultado de las anomal\u00edas estructurales de la cara, muchos pacientes tendr\u00e1n dificultades funcionales, como dificultad para alimentarse o comer, as\u00ed como dificultades para hablar. El subdesarrollo o la ausencia del canal auditivo y de las estructuras del o\u00eddo medio pueden provocar deficiencias o p\u00e9rdida de la audici\u00f3n, mientras que las anomal\u00edas del ojo pueden afectar la visi\u00f3n o incluso provocar la p\u00e9rdida de la visi\u00f3n. Los quistes dermoides epibulbares pueden causar m\u00e1s problemas de visi\u00f3n, como astigmatismo, ambliop\u00eda (ojo perezoso) y estrabismo (ojos cruzados).<\/p>\n<h2>Anomal\u00edas extracraneales<\/h2>\n<p>Aparte de las anomal\u00edas faciales, hasta el 55% de los pacientes con microsom\u00eda craneofacial pueden tener anomal\u00edas extracraneales. Por ejemplo, los pacientes que a menudo reciben el diagn\u00f3stico de s\u00edndrome de Goldenhar tendr\u00e1n anomal\u00edas en la columna vertebral y la caja tor\u00e1cica. Algunas personas experimentan una formaci\u00f3n incompleta de la columna vertebral y\/o la caja tor\u00e1cica, fusiones \u00f3seas anormales o falta de costillas o v\u00e9rtebras espinales. El problema m\u00e1s com\u00fan es la escoliosis cong\u00e9nita, una columna anormalmente curvada, que afecta hasta al 50% de los pacientes con s\u00edndrome de Goldenhar. El desarrollo anormal de la columna vertebral o las costillas tambi\u00e9n puede conducir a un crecimiento deficiente y limitar el desarrollo y la funci\u00f3n pulmonar. Algunos pacientes desarrollan s\u00edndrome de insuficiencia tor\u00e1cica, que impide la respiraci\u00f3n normal y la oxigenaci\u00f3n adecuada del organismo en casos graves.<\/p>\n<p>Otros \u00f3rganos, incluidos el coraz\u00f3n, los pulmones, los ri\u00f1ones y el sistema nervioso central, tambi\u00e9n pueden verse afectados en personas con microsom\u00eda craneofacial. De hecho, se ha observado que la presencia de manifestaciones extracraneales puede correlacionarse con una mayor severidad de los rasgos faciales. Las anomal\u00edas extracraneales espec\u00edficas incluyen:<\/p>\n<ul>\n<li>Defectos card\u00edacos cong\u00e9nitos<\/li>\n<li>Malformaciones renales (p. ej., ri\u00f1ones subdesarrollados o incluso la falta de un ri\u00f1\u00f3n en un lado)<\/li>\n<li>Malformaciones en las extremidades (p. ej., pie zambo, malformaciones en las manos)<\/li>\n<li>Hidrocefalia (acumulaci\u00f3n de l\u00edquido en los espacios ventriculares del cerebro)<\/li>\n<li>Apnea obstructiva del sue\u00f1o (obstrucci\u00f3n de la parte posterior de la garganta por tejidos blandos, incluidos el paladar blando, las am\u00edgdalas y la lengua, que provoca el cese intermitente de la respiraci\u00f3n y una disminuci\u00f3n de la oxigenaci\u00f3n durante el sue\u00f1o)<\/li>\n<li>Discapacidades intelectuales<\/li>\n<li>S\u00edntomas del espectro autista<\/li>\n<\/ul>\n\n\t\t<\/div>\n\t<\/div>\n<\/div><\/div><\/div><div class=\"wpb_column vc_column_container vc_col-sm-4\"><div class=\"vc_column-inner\"><div class=\"wpb_wrapper\"><div class=\"ult_row_spacer\"><div class=\"ult-sticky-anchor\"><div class=\"ult-sticky-section ult-sticky\"  data-gutter= '40' data-stick_behaviour= 'stick_with_scroll_row'  data-sticky_position= 'top' data-mobile='no' data-support='no'>\n\t<div class=\"wpb_text_column wpb_content_element\" >\n\t\t<div class=\"wpb_wrapper\">\n\t\t\t<h3 style=\"color: #d8007e;\">Recursos para la Comunidad Craneofacial<\/h3>\n<p>myFace proporciona a las personas y familias que viven con una diferencia facial acceso a atenci\u00f3n integral hol\u00edstica, servicios psicosociales, educaci\u00f3n, recursos y apoyo que allanan el camino para mejores resultados.<\/p>\n<h4><span style=\"text-decoration: underline;\"><a href=\"\/es\/events\/\">Pr\u00f3ximos eventos<\/a><\/span><\/h4>\n<h4><span style=\"text-decoration: underline;\"><a href=\"\/es\/civa\/\">Simuladores de cirug\u00eda 3D<\/a><\/span><\/h4>\n<h4><span style=\"text-decoration: underline;\"><a href=\"\/es\/parent-guides\/\">Las gu\u00edas para padres<\/a><\/span><\/h4>\n<h4><span style=\"text-decoration: underline;\"><a href=\"\/es\/online-groups\/\">Grupos de apoyo<\/a><\/span><\/h4>\n\n\t\t<\/div>\n\t<\/div>\n<\/div><div class=\"ult-space\"><\/div><\/div><\/div><\/div><\/div><\/div><\/div><\/div><\/div><\/div><\/div>\n<\/div>","protected":false},"excerpt":{"rendered":"<p><a class=\"sd-more sd-all-trans\" href=\"https:\/\/www.myface.org\/es\/craniofacial-conditions\/craniofacial-microsomia\/signs-symptoms\/#more-16552\">Leer m\u00e1s<\/a><\/p>","protected":false},"author":14,"featured_media":0,"parent":16528,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"full-width-page.php","meta":{"footnotes":""},"class_list":["post-16552","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.3 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Signs &amp; 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